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Diseases

Genetic and Rare Diseases Information Center (GARD)

Dermatofibrosarcoma protuberans


Other Names for this Disease
  • DFSP
  • Giant cell fibroblastoma
  • Familial dermatofibrosarcoma protuberans (subtype)
  • Metastatic dermatofibrosarcoma protuberans (subtype)
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Overview

Dermatofibrosarcoma protuberans is an uncommon cancer in which tumors arise in the deeper layers of skin. The tumor usually starts as a small, firm patch of skin; it may be purplish, reddish, or flesh-colored. It is commonly found on the torso, usually in the shoulder and chest area. The tumor typically grows slowly but has a tendency to recur after being removed. It rarely spreads to other parts of the body. The cause of DFSP is unknown, but injury to the affected skin may be a predisposing factor. Treatment usually involves surgically removing the tumor. If the tumor is unable to be removed completely, additional therapy may be needed. Regular follow-up is important to monitor for recurrence.[1][2][3]
Last updated: 2/9/2016

References

  1. Dermatofibrosarcoma protuberans. DermNet New Zealand Trust. September, 2015; http://www.dermnetnz.org/lesions/dfsp.html. Accessed 2/9/2016.
  2. Dermatofibrosarcoma Protuberans. Genetics Home Reference. September, 2011; http://ghr.nlm.nih.gov/condition/dermatofibrosarcoma-protuberans. Accessed 2/9/2016.
  3. Chen, Chih-Shan Jason. Dermatofibrosarcoma protuberans. Medscape Reference. November, 2015; http://emedicine.medscape.com/article/1100203-overview. Accessed 2/9/2016.
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Basic Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • Genetics Home Reference (GHR) contains information on Dermatofibrosarcoma protuberans. This website is maintained by the National Library of Medicine.

In Depth Information

  • Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free.
  • MeSH® (Medical Subject Headings) is a terminology tool used by the National Library of Medicine. Click on the link to view information on this topic.
  • Online Mendelian Inheritance in Man (OMIM) is a catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Dermatofibrosarcoma protuberans. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • DFSP
  • Giant cell fibroblastoma
  • Familial dermatofibrosarcoma protuberans (subtype)
  • Metastatic dermatofibrosarcoma protuberans (subtype)
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.