Other Names for this Disease
- Vacuolar cardiomyopathy and myopathy X-linked
- X-linked vacuolar cardiomyopathy and myopathy
- Antopol disease
- Pseudoglycogenosis 2
- Glycogen storage disease limited to the heart
On this page
Because Danon disease can be associated with rapidly progressive cardiomyopathy and sudden death, careful monitoring of heart disease is required. Aggressive interventions may be recommended for people showing signs of progressive heart failure (e.g., early intervention with heart transplantation or implantable cardioverter-defibrillator). However, the severity of cardiomyopathy does vary, particularly in females. Management will depend on the presence and severity of the heart disease, and will be tailored to the needs of the patient.
Last updated: 3/19/2010
- Finding Treatment Information - A video developed by GARD Information Specialists that explains how you can find information about treatment for a rare disease.
- Orphanet lists European clinical trials, research studies, and patient registries enrolling people with this condition.