Your browser does not support javascript:   Search for gard hereSearch for news-and-events here.

Diseases

Genetic and Rare Diseases Information Center (GARD)

Pityriasis lichenoides et varioliformis acuta


Other Names for this Disease
  • Mucha-Habermann disease
  • PLEVA
Related Diseases
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Your Question

How often does pityriasis lichenoides et varioliformis acuta turn into something more serious?

Our Answer

We have identified the following information that we hope you find helpful. If you still have questions, please contact us.

How often does pityriasis lichenoides et varioliformis acuta turn into something more serious?

Pityriasis lichenoides et varioliformis acuta (PLEVA) may evolve into cutaneous lymphoma in less than 2% of cases.

Rarely, a severe variant of PLEVA called febrile ulceronecrotic Mucha-Habermann disease (FUMHD) develops. FUMHD often begins as PLEVA, but then rapidly and suddenly progresses to large, destructive ulcers. There may be fever and extensive, painful loss of skin tissue. Patients may develop complications such as interstitial pneumonitis, abdominal pain, central nervous system involvement, bacteremia, and sepsis.[8204] For more information on this condition, please click here.
Last updated: 2/3/2015

References
Other Names for this Disease
  • Mucha-Habermann disease
  • PLEVA
Related Diseases
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.