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Diseases

Genetic and Rare Diseases Information Center (GARD)

Pityriasis lichenoides et varioliformis acuta


Other Names for this Disease
  • Mucha-Habermann disease
  • PLEVA
Related Diseases
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Symptoms

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What are the signs and symptoms of pityriasis lichenoides et varioliformis acuta?

Pityriasis lichenoides et varioliformis acuta (PLEVA) is the acute form of a skin condition called pityriasis lichenoides. It is characterized by the sudden onset of red patches that quickly develop into scaling papules. These papules may become filled with blood and/or pus or erode into crusted red-brown spots. People may also experience burning and itching of the affected area. Scarring and/or temporary discoloration of the skin may be present after the lesions have healed.[1][2][3]

Although PLEVA can affect almost any part of the body, it most commonly develops on the trunk and/or limbs (arms/legs). Affected people may have a few to more than one hundred papules. The skin abnormalities generally resolve without treatment in a few weeks to a few months; however, some people experience episodes of the condition on and off for years.[2][3]

Aside from the skin findings, most affected people do not experience any additional signs and symptoms. However, some may experience fever, headaches, joint pain and swelling of nearby lymph nodes.[2]

Febrile Ulceronecrotic Mucha-Haberman Disease is a rare and severe variant of PLEVA that is associated with unique signs and symptoms.[1][2] For more information on this condition, please click here.
Last updated: 2/2/2015

References
  1. Pityriasis lichenoides. DermNet NZ. January 2015; http://dermnetnz.org/scaly/pityriasis-lichenoides.html.
  2. Mucha Habermann disease. NORD. February 2012; http://www.rarediseases.org/rare-disease-information/rare-diseases/byID/752/viewAbstract.
  3. Peter A Klein, MD. Pityriasis Lichenoides. Medscape Reference. October 2014; http://emedicine.medscape.com/article/1099078-overview.


Other Names for this Disease
  • Mucha-Habermann disease
  • PLEVA
Related Diseases
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.