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Diseases

Genetic and Rare Diseases Information Center (GARD)

Amyopathic dermatomyositis


Other Names for this Disease
  • ADM
  • Dermatomyositis sine myositis
  • DM
  • Dermatomyositis
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Overview

Amyopathic dermatomyositis is a form of dermatomyositis characterized by the presence of typical skin findings without muscle weakness.[1][2] Some of the skin changes that suggest dermatomyositis include a pink rash on the face, neck, forearms and upper chest; Gottron's papules and heliotrope eyelids.[2][3][4] Pruritis and photosensitivity are common, as is scalp inflammation and thinning of the hair.[2][3] While patients with amyopathic dermatomyositis should not have clinically evident muscle weakness, minor muscle abnormalities may be included. Fatigue is reported in at least 50% of patients.[2] Some cases have been associated with internal malignancy and/or interstitial lung disease.[5] Treatment may include sun avoidance, ample use of sunscreen, topical corticosteroids, antimalarial agents, methotrexate, mycophenolate mofetil, or intravenous (IV) immunoglobulin.[1]
Last updated: 1/10/2013

References

  1. Callen JP. Dermatomyositis. Medscape Reference. October 2011; http://emedicine.medscape.com/article/332783-overview. Accessed 1/10/2013.
  2. Olsen NJ, Park JH, King LE Jr. Amyopathic dermatomyositis. Curr Rheumatol Rep. Aug 2001; http://www.ncbi.nlm.nih.gov/pubmed/11470054. Accessed 1/10/2012.
  3. Dermatomyositis. DermNet NZ. 2011; http://www.dermnetnz.org/immune/dermatomyositis.html. Accessed 1/10/2013.
  4. Saoud B, Allali F, Hassouni NH. Amyopathic dermatomyositis. Joint Bone Spine. May 2006; http://www.ncbi.nlm.nih.gov/pubmed/16253536. Accessed 1/10/2013.
  5. Sato S, Kuwana M. Clinically amyopathic dermatomyositis. Curr Opin Rheumatol. Nov 2010; http://www.ncbi.nlm.nih.gov/pubmed/20827200. Accessed 1/10/2013.
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Basic Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • Medscape Reference provides information on this topic. You may need to register to view the medical textbook, but registration is free.
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs. Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Amyopathic dermatomyositis. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • ADM
  • Dermatomyositis sine myositis
  • DM
  • Dermatomyositis
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.